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乙酰輔酶A酰基轉(zhuǎn)移酶1重組兔單抗

簡要描述:This gene encodes a mitochondrially localized enzyme that catalyzes the reversible formation of acetoacetyl-CoA from two molecules of acetyl-CoA. Defects in this gene are associated with 3-ketothiolase deficiency, an inborn error of isoleucine catabolism characterized by urinary excretion of 2-methyl-3-hydroxybutyric acid, 2-methylacetoacetic acid, tiglylglycine, and butanone. [provided by RefSeq, Feb 2009].

  • 產(chǎn)品型號:bsm-62678R
  • 廠商性質(zhì):生產(chǎn)廠家
  • 更新時間:2025-03-04
  • 訪  問  量: 129

詳細介紹

Human,Mouse,Rat
WB,IHC-P,IHC-F,IP,IF
Store at 4℃ for short term. Store at -20℃ for long term. Avoid repeated freeze/thaw cycles.

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